The JBJS Quiz of the Month is a collection of 10 relevant questions from each orthopaedic subspecialty. The questions are drawn from JBJS Clinical Classroom, which houses over 4,500 questions and 3,100 learning resources. Take the Quiz to see how you score against your peers!

NOTE: This quiz does not earn users CME credits. The questions must be answered within Clinical Classroom to earn CME credits.

A 14-year-old male patient recently diagnosed with a defect in chromosome 9q13 related to the trinucleotide repeat GAA is referred for scoliosis evaluation. He walks with a slightly wide-based gait and has absent deep tendon reflexes. On examination, he has bilateral rigid cavovarus feet. Posteroanterior scoliosis radiographs reveal a major curve with a Cobb angle of 30°. Which of the following is the most appropriate treatment for his scoliosis?
    • Posterior spinal fusion with instrumentation
    • The description is that is that of Friedreich ataxia. Scoliosis is associated, but at 30° can be observed.
    • Growing rod spinal instrumentation with delayed spinal fusion
    • Growing rods are utilized for a younger age and a more severe curve.
    • Observation with possible bracing
    • The description is that is that of Friedreich ataxia. Scoliosis is associated, but at 30° can be observed and possibly braced.
    • Combined anterior/posterior spinal fusion with instrumentation
    • The description is that is that of Friedreich ataxia. Scoliosis is associated, but at 30° can be observed and possibly braced.

     

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